Maple Syrup Urine Disease

Have you ever heard of this serious disease? I use maple syrup very often as a sugar substitute.

"Maple syrup urine disease (MSUD) was first described in 1954 by pediatrician John Menkes et al. The disease was named after the maple syrup-like odor of the urine." (Google search AI result)

"People with maple syrup urine disease (MSUD) can’t break down three specific amino acids found in protein-containing foods. These amino acids build up, become toxic and cause severe health problems. Without medical management, MSUD can lead to a wide range of intellectual and physical disabilities. It can be fatal without proper management."

Maple Syrup Urine Disease: What It Is, Symptoms & Treatment